Budd Chiari Syndrome

Budd-Chiari syndrome (BCS) represents obstruction of hepatic venous drainage. The site of obstruction may be anywhere from the small central lobar veins of the liver to the proximal
inferior vena cava (IVC). Protein C is the zymogen of a vitamin K-dependent involved in blood coagulation. Protein C deficieny is an autosomal dominant disorder. This condition
promote excessive fibrin formation and thus constitute a risk factor for thrombosis. We report the case of a female patient who was protein C deficiency had severe thrombotic complications.

Budd Chiari Sendromu