. 1999; 5(2): 132-133 | |||
PEUTZ JEGHERS SENDROMUAhmet Yılmaz1, Kadri Güler1, Hakan Bozkurtoğlu1, Faik Çelik1SSK Göztepe Eğitim Hastanesi 4. Cerrahi KliniğiPEUTZ JEGHERS SYNDROMEAhmet Yılmaz1, Kadri Güler1, Hakan Bozkurtoğlu1, Faik Çelik1SSK Göztepe Eğitim Hastanesi 4. Cerrahi KliniğiPeutz - Jeghers Syndrome is a rare, inherited autozomal dominant disease characterized by gastrointestinal hamartomatous polyps and mucocutaneous pigmentation. In this paper we report two cases of Peutz -Jeghers syndrome who were admitted and operated with intussusception. Screening their family members revealed intestinal and extraintestinal manifestations of the disease and no malignancy was detected. Keywords: PEUTZ-JEGHERS SYNDROME, INTUSSUSCEPTIONAhmet Yılmaz, Kadri Güler, Hakan Bozkurtoğlu, Faik Çelik. PEUTZ JEGHERS SYNDROME. . 1999; 5(2): 132-133 |
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