. 1999; 5(2): 132-133

PEUTZ JEGHERS SENDROMU

Ahmet Yılmaz1, Kadri Güler1, Hakan Bozkurtoğlu1, Faik Çelik1
SSK Göztepe Eğitim Hastanesi 4. Cerrahi Kliniği



PEUTZ JEGHERS SYNDROME

Ahmet Yılmaz1, Kadri Güler1, Hakan Bozkurtoğlu1, Faik Çelik1
SSK Göztepe Eğitim Hastanesi 4. Cerrahi Kliniği

Peutz - Jeghers Syndrome is a rare, inherited autozomal dominant disease characterized by gastrointestinal hamartomatous polyps and mucocutaneous pigmentation. In this paper we report two cases of Peutz -Jeghers syndrome who were admitted and operated with intussusception. Screening their family members revealed intestinal and extraintestinal manifestations of the disease and no malignancy was detected.

Keywords: PEUTZ-JEGHERS SYNDROME, INTUSSUSCEPTION


Ahmet Yılmaz, Kadri Güler, Hakan Bozkurtoğlu, Faik Çelik. PEUTZ JEGHERS SYNDROME. . 1999; 5(2): 132-133


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