. 2020; 37(3): 139-144 | DOI: 10.4274/tjh.galenos.2020.2019.0380 | |||
İmmün Trombositopenili Çocuk Hastalarda Eltrombopag Tedavisi ve Tedaviye Bağlı Demir EksikliğiAyça Koca Yozgat1, Göksel Leblebisatan2, Sinan Akbayram3, Simge Çınar Özel4, Zeynep Karakaş5, Erol Erduran6, Şebnem Yılmaz7, Ülker Koçak8, Şule Ünal9, Gül Nihal Özdemir10, Meryem Albayrak11, Emine Zengin12, Yeşim Oymak13, Özcan Bör14, Hasan Fatih Çakmaklı15, Murat Söker16, Dilek Gürlek Gökçebay17, Hüseyin Tokgöz18, Barış Malbora19, Serap Karaman5, Tiraje Celkan4, İlgen Şaşmaz2, Neşe Yaralı1, Hale Ören7, Ayşegül Ünüvar51Ankara City Hospital, Clinic of Pediatric Hematology, Ankara, Turkey2Çukurova University Faculty of Medicine, Department of Pediatric Hematology, Adana, Turkey 3Gaziantep University Faculty of Medicine, Department of Pediatric Hematology, Gaziantep, Turkey 4İstanbul University-Cerrahpaşa Cerrahpaşa Faculty of Medicine, Department of Pediatric Hematology, İstanbul, Turkey 5İstanbul University, İstanbul Faculty of Medicine, Department of Pediatric Hematology, İstanbul, Turkey 6Karadeniz Technical University Faculty of Medicine, Department of Pediatric Hematology, Trabzon, Turkey 7Dokuz Eylül University Faculty of Medicine, Department of Pediatric Hematology, İzmir, Turkey 8Gazi University Faculty of Medicine, Department of Pediatric Hematology, Ankara, Turkey 9Hacettepe University Faculty of Medicine, Department of Pediatric Hematology, Ankara, Turkey 10Kanuni Sultan Süleyman Training and Research Hospital, Clinic of Pediatric Hematology, İstanbul, Turkey 11Kırıkkale University Faculty of Medicine, Department of Pediatric Hematology, Kırıkkale, Turkey 12Kocaeli University Faculty of Medicine, Department of Pediatric Hematology, Kocaeli, Turkey 13Dr. Behçet Uz Children’s Training and Research Hospital, Clinic of Pediatric Hematology, İzmir, Turkey 14Eskişehir University Faculty of Medicine, Department of Pediatric Hematology, Eskişehir, Turkey 15Ankara University Faculty of Medicine, Department of Pediatric Hematology, Ankara, Turkey 16Dicle University Faculty of Medicine, Department of Pediatric Hematology, Diyarbakır, Turkey 17Ankara Keçiören Training and Research Hospital, Clinic of Pediatric Hematology, Ankara, Turkey 18Necmettin Erbakan University Meram Faculty of Medicine, Department of Pediatric Hematology, Konya, Turkey 19Yeni Yüzyıl University, Gaziosmanpaşa Hospital, Clinic of Pediatric Hematology, İstanbul, Turkey Amaç: İmmün trombositopeni (İTP) nadir otoimmün bir hastalık olup, platelet sayısındaki azalmaya bağlı olarak peteşi, ekimoz, epistaksis gibi kanama semptomları ile karakterizedir. Trombopoietin reseptör agonisti eltrombopag (EPAG), yetişkinlerde ve çocuklarda kronik immün trombositopeni tedavisinde kullanılan ikinci basamak bir ajandır. Outcomes of Eltrombopag Treatment and Development of Iron Deficiency in Children with Immune Thrombocytopenia in TurkeyAyça Koca Yozgat1, Göksel Leblebisatan2, Sinan Akbayram3, Simge Çınar Özel4, Zeynep Karakaş5, Erol Erduran6, Şebnem Yılmaz7, Ülker Koçak8, Şule Ünal9, Gül Nihal Özdemir10, Meryem Albayrak11, Emine Zengin12, Yeşim Oymak13, Özcan Bör14, Hasan Fatih Çakmaklı15, Murat Söker16, Dilek Gürlek Gökçebay17, Hüseyin Tokgöz18, Barış Malbora19, Serap Karaman5, Tiraje Celkan4, İlgen Şaşmaz2, Neşe Yaralı1, Hale Ören7, Ayşegül Ünüvar51Ankara City Hospital, Clinic of Pediatric Hematology, Ankara, Turkey2Çukurova University Faculty of Medicine, Department of Pediatric Hematology, Adana, Turkey 3Gaziantep University Faculty of Medicine, Department of Pediatric Hematology, Gaziantep, Turkey 4İstanbul University-Cerrahpaşa Cerrahpaşa Faculty of Medicine, Department of Pediatric Hematology, İstanbul, Turkey 5İstanbul University, İstanbul Faculty of Medicine, Department of Pediatric Hematology, İstanbul, Turkey 6Karadeniz Technical University Faculty of Medicine, Department of Pediatric Hematology, Trabzon, Turkey 7Dokuz Eylül University Faculty of Medicine, Department of Pediatric Hematology, İzmir, Turkey 8Gazi University Faculty of Medicine, Department of Pediatric Hematology, Ankara, Turkey 9Hacettepe University Faculty of Medicine, Department of Pediatric Hematology, Ankara, Turkey 10Kanuni Sultan Süleyman Training and Research Hospital, Clinic of Pediatric Hematology, İstanbul, Turkey 11Kırıkkale University Faculty of Medicine, Department of Pediatric Hematology, Kırıkkale, Turkey 12Kocaeli University Faculty of Medicine, Department of Pediatric Hematology, Kocaeli, Turkey 13Dr. Behçet Uz Children’s Training and Research Hospital, Clinic of Pediatric Hematology, İzmir, Turkey 14Eskişehir University Faculty of Medicine, Department of Pediatric Hematology, Eskişehir, Turkey 15Ankara University Faculty of Medicine, Department of Pediatric Hematology, Ankara, Turkey 16Dicle University Faculty of Medicine, Department of Pediatric Hematology, Diyarbakır, Turkey 17Ankara Keçiören Training and Research Hospital, Clinic of Pediatric Hematology, Ankara, Turkey 18Necmettin Erbakan University Meram Faculty of Medicine, Department of Pediatric Hematology, Konya, Turkey 19Yeni Yüzyıl University, Gaziosmanpaşa Hospital, Clinic of Pediatric Hematology, İstanbul, Turkey Objective: Immune thrombocytopenia (ITP) is a rare autoimmune disease and hematologic disorder characterized by reduced platelet counts that can result in significant symptoms, such as bleeding, bruising, epistaxis, or petechiae. The thrombopoietin receptor agonist eltrombopag (EPAG) is a second-line agent used to treat chronic ITP purpura in adults and children. Ayça Koca Yozgat, Göksel Leblebisatan, Sinan Akbayram, Simge Çınar Özel, Zeynep Karakaş, Erol Erduran, Şebnem Yılmaz, Ülker Koçak, Şule Ünal, Gül Nihal Özdemir, Meryem Albayrak, Emine Zengin, Yeşim Oymak, Özcan Bör, Hasan Fatih Çakmaklı, Murat Söker, Dilek Gürlek Gökçebay, Hüseyin Tokgöz, Barış Malbora, Serap Karaman, Tiraje Celkan, İlgen Şaşmaz, Neşe Yaralı, Hale Ören, Ayşegül Ünüvar. Outcomes of Eltrombopag Treatment and Development of Iron Deficiency in Children with Immune Thrombocytopenia in Turkey. . 2020; 37(3): 139-144 Sorumlu Yazar: Ayça Koca Yozgat, Türkiye |
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