. 2022; 39(2): 130-135 | DOI: 10.4274/tjh.galenos.2022.2021.0670 | |||
Castleman Hastalığı: Türkiye’den Çok Merkezli Bir Olgu SerisiEren Gündüz1, Hakkı Onur Kırkızlar2, Elif Gülsüm Ümit2, Sedanur Karaman Gülsaran2, Vildan Özkocaman3, Fahir Özkalemkaş3, Ömer Candar3, Tugrul Elverdi4, Selin Küçükyurt4, Semra Paydaş5, Özcan Çeneli6, Sema Karakuş7, Senem Maral8, Ömer Ekinci9, Yıldız İpek10, Cem Kis11, Zeynep Tuğba Güven12, Aydan Akdeniz13, Tiraje Celkan14, Ayşe Hilal Eroğlu Küçükdiler15, Gülsüm Akgün Çağlıyan16, Ceyda Özçelik Şengöz17, Ayşe Karataş18, Tuba Bulduk19, Alper Özcan12, Fatma Burcu Belen Apak7, Aylin Canbolat20, İbrahim Kartal21, Hale Ören22, Ersin Töret1, Gül Nihal Özdemir14, Şule Mine Bakanay Öztürk231Eskişehir Osmangazi University Faculty of Medicine, Department of Hematology, Eskişehir, Turkey2Trakya University Faculty of Medicine, Department of Hematology, Edirne, Turkey 3Uludağ University Faculty of Medicine, Department of Hematology, Bursa, Turkey 4İstanbul University-Cerrahpaşa Cerrahpaşa Faculty of Medicine, Department of Hematology, İstanbul, Turkey 5Çukurova University Faculty of Medicine, Department of Hematology, Adana, Turkey 6Necmettin Erbakan University Meram Faculty of Medicine, Department of Hematology, Konya, Turkey 7Ankara Başkent University Faculty of Medicine, Department of Hematology, Ankara, Turkey 8University of Health Sciences Turkey Ankara Dışkapı Yıldırım Beyazıt Training and Research Hospital, Clinic of Hematology, Ankara, Turkey 9Fırat University Faculty of Medicine, Department of Hematology, Elazığ, Turkey 10Kartal Dr. Lütfi Kırdar City Hospital, Clinic of Hematology, İstanbul, Turkey 11Adana Başkent University Faculty of Medicine, Department of Hematology, Adana, Turkey 12Erciyes University Faculty of Medicine, Department of Hematology, Kayseri, Turkey 13Mersin University Faculty of Medicine, Department of Hematology, Mersin, Turkey 14İstinye University Faculty of Medicine, Department of Pediatric Hematology, İstanbul, Turkey 15Adnan Menderes University Faculty of Medicine, Department of Hematology, Aydın, Turkey 16Pamukkale University Faculty of Medicine, Department of Hematology, Denizli, Turkey 17Karadeniz Technical University Faculty of Medicine, Department of Hematology, Trabzon, Turkey 18Hacettepe University Faculty of Medicine, Department of Hematology, Ankara, Turkey 19University of Health Sciences Turkey Gülhane Training and Research Hospital, Clinic of Hematology, Ankara, Turkey 20İstanbul Medeniyet University Faculty of Medicine, Department of Pediatric Hematology, İstanbul, Turkey 21Ondokuz Mayıs University Faculty of Medicine, Department of Pediatric Hematology, Samsun, Turkey 22Dokuz Eylül University Faculty of Medicine, Department of Pediatric Hematology, İzmir, Turkey 23Ankara Yıldırım Beyazıt University Faculty of Medicine, Department of Hematology, Ankara, Turkey Amaç: Anjiyofolliküler lenf nodu hiperplazisi olarak da bilinen Castleman hastalığı (CH), nadir bir hastalık olup başlıca hiyalin vasküler ve plazma hücreli olmak üzere 2 histolojik alt tipi vardır. Hastalığın anatomik yayılımı ve tutulan lenf nodu bölgelerinin sayısına göre unisentrik (UCH) ya da multisentrik (MCH) olarak sınıflandırılır. Bu çok merkezli çalışmanın amacı bugüne kadar Türkiye’de tanımlanan tüm CH olgularını tanımlamak, ulusal bir veri tabanı oluşturarak CH’de erken tanı, tedavi ve takip sürecine katkı sağlamaktır. Castleman Disease: A Multicenter Case Series from TurkeyEren Gündüz1, Hakkı Onur Kırkızlar2, Elif Gülsüm Ümit2, Sedanur Karaman Gülsaran2, Vildan Özkocaman3, Fahir Özkalemkaş3, Ömer Candar3, Tugrul Elverdi4, Selin Küçükyurt4, Semra Paydaş5, Özcan Çeneli6, Sema Karakuş7, Senem Maral8, Ömer Ekinci9, Yıldız İpek10, Cem Kis11, Zeynep Tuğba Güven12, Aydan Akdeniz13, Tiraje Celkan14, Ayşe Hilal Eroğlu Küçükdiler15, Gülsüm Akgün Çağlıyan16, Ceyda Özçelik Şengöz17, Ayşe Karataş18, Tuba Bulduk19, Alper Özcan12, Fatma Burcu Belen Apak7, Aylin Canbolat20, İbrahim Kartal21, Hale Ören22, Ersin Töret1, Gül Nihal Özdemir14, Şule Mine Bakanay Öztürk231Eskişehir Osmangazi University Faculty of Medicine, Department of Hematology, Eskişehir, Turkey2Trakya University Faculty of Medicine, Department of Hematology, Edirne, Turkey 3Uludağ University Faculty of Medicine, Department of Hematology, Bursa, Turkey 4İstanbul University-Cerrahpaşa Cerrahpaşa Faculty of Medicine, Department of Hematology, İstanbul, Turkey 5Çukurova University Faculty of Medicine, Department of Hematology, Adana, Turkey 6Necmettin Erbakan University Meram Faculty of Medicine, Department of Hematology, Konya, Turkey 7Ankara Başkent University Faculty of Medicine, Department of Hematology, Ankara, Turkey 8University of Health Sciences Turkey Ankara Dışkapı Yıldırım Beyazıt Training and Research Hospital, Clinic of Hematology, Ankara, Turkey 9Fırat University Faculty of Medicine, Department of Hematology, Elazığ, Turkey 10Kartal Dr. Lütfi Kırdar City Hospital, Clinic of Hematology, İstanbul, Turkey 11Adana Başkent University Faculty of Medicine, Department of Hematology, Adana, Turkey 12Erciyes University Faculty of Medicine, Department of Hematology, Kayseri, Turkey 13Mersin University Faculty of Medicine, Department of Hematology, Mersin, Turkey 14İstinye University Faculty of Medicine, Department of Pediatric Hematology, İstanbul, Turkey 15Adnan Menderes University Faculty of Medicine, Department of Hematology, Aydın, Turkey 16Pamukkale University Faculty of Medicine, Department of Hematology, Denizli, Turkey 17Karadeniz Technical University Faculty of Medicine, Department of Hematology, Trabzon, Turkey 18Hacettepe University Faculty of Medicine, Department of Hematology, Ankara, Turkey 19University of Health Sciences Turkey Gülhane Training and Research Hospital, Clinic of Hematology, Ankara, Turkey 20İstanbul Medeniyet University Faculty of Medicine, Department of Pediatric Hematology, İstanbul, Turkey 21Ondokuz Mayıs University Faculty of Medicine, Department of Pediatric Hematology, Samsun, Turkey 22Dokuz Eylül University Faculty of Medicine, Department of Pediatric Hematology, İzmir, Turkey 23Ankara Yıldırım Beyazıt University Faculty of Medicine, Department of Hematology, Ankara, Turkey Objective: Castleman disease (CD) is a rare disease also known as angiofollicular lymph node hyperplasia. The two main histological subtypes are the hyaline vascular and plasma cell variants. It is further classified as unicentric CD (UCD) or multicentric CD (MCD) according to the anatomical distribution of the disease and the number of lymph nodes involved. The aim of this multicenter study was to evaluate all cases of CD identified to date in Turkey to set up a national registry to improve the early recognition, treatment, and follow-up of CD. Eren Gündüz, Hakkı Onur Kırkızlar, Elif Gülsüm Ümit, Sedanur Karaman Gülsaran, Vildan Özkocaman, Fahir Özkalemkaş, Ömer Candar, Tugrul Elverdi, Selin Küçükyurt, Semra Paydaş, Özcan Çeneli, Sema Karakuş, Senem Maral, Ömer Ekinci, Yıldız İpek, Cem Kis, Zeynep Tuğba Güven, Aydan Akdeniz, Tiraje Celkan, Ayşe Hilal Eroğlu Küçükdiler, Gülsüm Akgün Çağlıyan, Ceyda Özçelik Şengöz, Ayşe Karataş, Tuba Bulduk, Alper Özcan, Fatma Burcu Belen Apak, Aylin Canbolat, İbrahim Kartal, Hale Ören, Ersin Töret, Gül Nihal Özdemir, Şule Mine Bakanay Öztürk. Castleman Disease: A Multicenter Case Series from Turkey. . 2022; 39(2): 130-135 Sorumlu Yazar: Eren Gündüz |
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