. 2021; 38(2): 101-110 | DOI: 10.4274/tjh.galenos.2021.2020.0717 | |||
Hemofili Hastalarında Profilaksinin Koruyucu Etkisinin Gözlenmesinde HEAD-US Skorlama Sisteminin Önemi: Prospektif, Çok Merkezli ve Gözlemsel Bir ÇalışmaKaan Kavaklı1, Süha Süreyya Özbek2, Ali Bülent Antmen3, Fahri Şahin4, Şevkiye Selin Aytaç5, Alphan Küpesiz6, Bülent Zülfikar7, Mehmet Sönmez8, Ümran Çalışkan9, Can Balkan1, Tuğana Akbaş10, Taner Arpacı10, İpek Tamsel2, Turgut Seber11, Berna Oğuz11, Can Çevikol12, Mesut Bulakçı7, Polat Koşucu13, Demet Aydoğdu14, İlgen Şaşmaz3, Gülen Tüysüz6, Başak Koç7, Hüseyin Tokgöz9, Zuhal Demirci4, Burcu Özkan151Ege University Children’s Hospital, Clinic of Children’s Health and Diseases, Division of Pediatric Hematology, İzmir, Turkey2Ege University Medical Faculty Hospital, Clinic of Radiology, Division of Hematology, İzmir, Turkey 3Acıbadem Adana Hospital, Clinic of Pediatric Hematology, Adana, Turkey 4Ege University Medical Faculty Hospital, Clinic of Internal Diseases, Division of Hematology, İzmir, Turkey 5Hacettepe University Faculty of Medicine, Department of Children’s Health and Diseases, Division of Pediatric Hematology, Ankara, Turkey 6Akdeniz University Hospital, Clinic of Children’s Health and Diseases, Antalya, Turkey 7İstanbul University Hemophilia Comprehensive Care Center, İstanbul, Turkey 8Karadeniz Technical University Medical Faculty Farabi Hospital, Clinic of Internal Diseases, Division of Hematology, Trabzon, Turkey 9Necmettin Erbakan University Meram Medical Faculty Hospital, Department of Children’s Health and Diseases, Konya, Turkey 10Acıbadem Adana Hospital, Clinic of Radiology, Adana, Turkey 11Hacettepe University Faculty of Medicine, Department of Radiology, Ankara, Turkey 12Akdeniz University Hospital, Clinic of Radiology, Antalya, Turkey 13Karadeniz Technical University Medical Faculty Farabi Hospital, Clinic of Radiology, Trabzon, Turkey 14Necmettin Erbakan University Meram Medical Faculty Hospital, Clinic of Radiology, Konya, Turkey 15Pfizer Pharmaceuticals, Rare Disease Department, İstanbul, Turkey Amaç: Bu çalışmada hemofili hastalarında profilaksinin eklem sağlığı üzerindeki koruyucu etkisini gözlemlemek ve eklemlerin klinik ve ultrasonografik olarak değerlendirilmesinin öneminin araştırılması amaçlandı. Impact of the HEAD-US Scoring System for Observing the Protective Effect of Prophylaxis in Hemophilia Patients: A Prospective, Multicenter, Observational StudyKaan Kavaklı1, Süha Süreyya Özbek2, Ali Bülent Antmen3, Fahri Şahin4, Şevkiye Selin Aytaç5, Alphan Küpesiz6, Bülent Zülfikar7, Mehmet Sönmez8, Ümran Çalışkan9, Can Balkan1, Tuğana Akbaş10, Taner Arpacı10, İpek Tamsel2, Turgut Seber11, Berna Oğuz11, Can Çevikol12, Mesut Bulakçı7, Polat Koşucu13, Demet Aydoğdu14, İlgen Şaşmaz3, Gülen Tüysüz6, Başak Koç7, Hüseyin Tokgöz9, Zuhal Demirci4, Burcu Özkan151Ege University Children’s Hospital, Clinic of Children’s Health and Diseases, Division of Pediatric Hematology, İzmir, Turkey2Ege University Medical Faculty Hospital, Clinic of Radiology, Division of Hematology, İzmir, Turkey 3Acıbadem Adana Hospital, Clinic of Pediatric Hematology, Adana, Turkey 4Ege University Medical Faculty Hospital, Clinic of Internal Diseases, Division of Hematology, İzmir, Turkey 5Hacettepe University Faculty of Medicine, Department of Children’s Health and Diseases, Division of Pediatric Hematology, Ankara, Turkey 6Akdeniz University Hospital, Clinic of Children’s Health and Diseases, Antalya, Turkey 7İstanbul University Hemophilia Comprehensive Care Center, İstanbul, Turkey 8Karadeniz Technical University Medical Faculty Farabi Hospital, Clinic of Internal Diseases, Division of Hematology, Trabzon, Turkey 9Necmettin Erbakan University Meram Medical Faculty Hospital, Department of Children’s Health and Diseases, Konya, Turkey 10Acıbadem Adana Hospital, Clinic of Radiology, Adana, Turkey 11Hacettepe University Faculty of Medicine, Department of Radiology, Ankara, Turkey 12Akdeniz University Hospital, Clinic of Radiology, Antalya, Turkey 13Karadeniz Technical University Medical Faculty Farabi Hospital, Clinic of Radiology, Trabzon, Turkey 14Necmettin Erbakan University Meram Medical Faculty Hospital, Clinic of Radiology, Konya, Turkey 15Pfizer Pharmaceuticals, Rare Disease Department, İstanbul, Turkey Objective: This study aimed to observe the preventive effect of prophylactic treatment on joint health in people with hemophilia (PwH) and to investigate the importance of integration of ultrasonographic examination into clinical and radiological evaluation of the joints. Kaan Kavaklı, Süha Süreyya Özbek, Ali Bülent Antmen, Fahri Şahin, Şevkiye Selin Aytaç, Alphan Küpesiz, Bülent Zülfikar, Mehmet Sönmez, Ümran Çalışkan, Can Balkan, Tuğana Akbaş, Taner Arpacı, İpek Tamsel, Turgut Seber, Berna Oğuz, Can Çevikol, Mesut Bulakçı, Polat Koşucu, Demet Aydoğdu, İlgen Şaşmaz, Gülen Tüysüz, Başak Koç, Hüseyin Tokgöz, Zuhal Demirci, Burcu Özkan. Impact of the HEAD-US Scoring System for Observing the Protective Effect of Prophylaxis in Hemophilia Patients: A Prospective, Multicenter, Observational Study. . 2021; 38(2): 101-110 Sorumlu Yazar: Kaan Kavaklı, Türkiye |
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