. 2022; 39(3): 170-177 | DOI: 10.4274/tjh.galenos.2022.2022.0052 | |||
Non-kutanöz Periferik T-hücreli Lenfomalarda Klinik Özellikler ve Tedavi Sonuçlarına ilişkin Gerçek Yaşam Deneyimi: Türk Hematoloji Araştırma ve Eğitim Grubunun Çok Merkezli ÇalışmasıÖmür Kayıkçı1, Özgür Mehtap2, İsmail Sarı3, Fatih Demirkan4, Cengiz Beyan5, Güven Çetin6, Filiz Vural7, Mehmet Yılmaz8, Erman Öztürk9, Seval Akpınar10, Bülent Eser11, Mehmet Gündüz12, Yahya Büyükaşık13, Bahriye Payzin14, Rahşan Yıldırım15, Mehmet Hilmi Doğu16, Atilla Özkan17, Engin Kelkitli18, Emre Tekgündüz11Memorial Bahçelievler Hospital, Clinic of Hematology, İstanbul, Turkey2Kocaeli University Faculty of Medicine, Department of Hematology, Kocaeli, Turkey 3Memorial Ataşehir Hospital, Clinic of Hematology, İstanbul, Turkey 4Dokuz Eylül University Faculty of Medicine, Division of Hematology, İzmir, Turkey 5Ufuk University Faculty of Medicine, Division of Hematology, Ankara, Turkey 6Bezmialem Vakıf University Faculty of Medicine, Department of Hematology, İstanbul, Turkey 7Ege University Faculty of Medicine, Department of Hematology, İzmir, Turkey 8Sanko University Faculty of Medicine, Department of Hematology, Gaziantep, Turkey 9Medeniyet University Training and Research Hospital, Clinic of Hematology, İstanbul, Turkey 10Namık Kemal University Faculty of Medicine, Department of Hematology, Tekirdağ, Turkey 11Medical Park Hospital, Clinic of Hematology, İstanbul, Turkey 12Biruni University Hospital, Clinic of Hematology, İstanbul, Turkey 13Hacettepe University Faculty of Medicine, Department of Hematology, Ankara, Turkey 14İzmir Katip Çelebi University Atatürk Training and Research Hospital, Clinic of Hematology, İzmir, Turkey 15İstinye University Faculty of Medicine, Department of Hematology, İstanbul, Turkey 16Liv Hospital, Clinic of Hematology, İstanbul, Turkey 17Yeditepe University Hospital, Clinic of Hematology, İstanbul, Turkey 18Ondokuz Mayıs University Faculty of Medicine, Department of Hematology, Samsun, Turkey Amaç: Periferik T-hücreli lenfomalar (PTHL) nadir görülen, oldukça heterojen bir grup hastalıktır ve tüm non-Hodgkin lenfomaların sadece %10-15’ini oluşturur. Son yıllarda hem moleküler hem de klinik çalışmalar artmış olsa da PTHL’ler üzerindeki gerçek yaşam verileri hakkında hala çok az bilgiye sahibiz. Bu çalışmada, sistemik, kutanöz olmayan PTHL hastaları içeren geniş popülasyon tabanlı hasta grubunun klinik özellikleri ve tedavi sonuçlarını araştırmayı amaçladık. Real-Life Experience Regarding Clinical Characteristics and Treatment Outcome in Non-Cutaneous Peripheral T-Cell Lymphomas: A Multicenter Study of the Turkish Hematology Research and Education Group (ThREG)Ömür Kayıkçı1, Özgür Mehtap2, İsmail Sarı3, Fatih Demirkan4, Cengiz Beyan5, Güven Çetin6, Filiz Vural7, Mehmet Yılmaz8, Erman Öztürk9, Seval Akpınar10, Bülent Eser11, Mehmet Gündüz12, Yahya Büyükaşık13, Bahriye Payzin14, Rahşan Yıldırım15, Mehmet Hilmi Doğu16, Atilla Özkan17, Engin Kelkitli18, Emre Tekgündüz11Memorial Bahçelievler Hospital, Clinic of Hematology, İstanbul, Turkey2Kocaeli University Faculty of Medicine, Department of Hematology, Kocaeli, Turkey 3Memorial Ataşehir Hospital, Clinic of Hematology, İstanbul, Turkey 4Dokuz Eylül University Faculty of Medicine, Division of Hematology, İzmir, Turkey 5Ufuk University Faculty of Medicine, Division of Hematology, Ankara, Turkey 6Bezmialem Vakıf University Faculty of Medicine, Department of Hematology, İstanbul, Turkey 7Ege University Faculty of Medicine, Department of Hematology, İzmir, Turkey 8Sanko University Faculty of Medicine, Department of Hematology, Gaziantep, Turkey 9Medeniyet University Training and Research Hospital, Clinic of Hematology, İstanbul, Turkey 10Namık Kemal University Faculty of Medicine, Department of Hematology, Tekirdağ, Turkey 11Medical Park Hospital, Clinic of Hematology, İstanbul, Turkey 12Biruni University Hospital, Clinic of Hematology, İstanbul, Turkey 13Hacettepe University Faculty of Medicine, Department of Hematology, Ankara, Turkey 14İzmir Katip Çelebi University Atatürk Training and Research Hospital, Clinic of Hematology, İzmir, Turkey 15İstinye University Faculty of Medicine, Department of Hematology, İstanbul, Turkey 16Liv Hospital, Clinic of Hematology, İstanbul, Turkey 17Yeditepe University Hospital, Clinic of Hematology, İstanbul, Turkey 18Ondokuz Mayıs University Faculty of Medicine, Department of Hematology, Samsun, Turkey Objective: Peripheral T-cell lymphomas (PTCLs) are an uncommon and quite heterogeneous group of disorders, representing only 10%-15% of all non-Hodgkin lymphomas. Although both molecular and clinical studies have increased in recent years, we still have little knowledge regarding real-life practice with PTCLs. In this study, we aimed to investigate the clinical characteristics and treatment outcomes of a large population-based cohort of patients presenting with systemic non-cutaneous PTCL. Ömür Kayıkçı, Özgür Mehtap, İsmail Sarı, Fatih Demirkan, Cengiz Beyan, Güven Çetin, Filiz Vural, Mehmet Yılmaz, Erman Öztürk, Seval Akpınar, Bülent Eser, Mehmet Gündüz, Yahya Büyükaşık, Bahriye Payzin, Rahşan Yıldırım, Mehmet Hilmi Doğu, Atilla Özkan, Engin Kelkitli, Emre Tekgündüz. Real-Life Experience Regarding Clinical Characteristics and Treatment Outcome in Non-Cutaneous Peripheral T-Cell Lymphomas: A Multicenter Study of the Turkish Hematology Research and Education Group (ThREG). . 2022; 39(3): 170-177 Sorumlu Yazar: Ömür Kayıkçı, Türkiye |
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